Dedifferentiated chondrosarcoma (n = 16) Frequency (%)
Age (years) † 62.5 (39-83)
Race
White 13 (81.3)
Other/Unknown 3 (18.8)
Sex
Male 7 (43.8)
Female 9 (56.3)
Location
Femur 8 (50)
Pelvis 4 (25)
Ribs 1 (6.3)
Periscapula 1 (6.3)
Tibia 1 (6.3)
Initial metastasis 3 (18.8)
Initial biopsy 14 (87.5)
Neoadjuvant chemotherapy 2 (12.5)
Neoadjuvant radiation 2 (12.5)
Surgery 14 (87.6)
Limb salvage/wide resection 13 (81.3)
Intralesional 1 (6.3)
Size (cm) ‡ 9.77 (5.02)
Negative margins
Yes 12 (75)
No 2 (12.5)
Missing 2 (12.5)
Dedifferentiated component
Osteosarcoma 5 (31.3)
UPS 6 (37.5)
Rhabdomyosarcoma 1 (6.3)
Low-grade dedifferentiation 1 (6.3)
Mixed 1 (6.3)
Reoperation 6 (37.5)
Adjuvant chemotherapy 5 (31.3)
Adjuvant radiation 7 (43.8)
Follow-up (months) † 18.5 (1-140)
Disease relapse 15 (93.8)
Mortality 13 (81.3)